定义:左心发育不良综合症(Hypoplastic left heart syndrome,HLHS)是一组先天性畸形,以不同程度的左心–主动脉复合体的发育不良(即主动脉、主动脉瓣、左室、二尖瓣和左房发育不良)、左心腔狭小、主动脉瓣口及二尖瓣口狭小或闭锁、升主动脉细小等为特征,导致体循环心脏输出梗阻以及左心无力承担体循环,发病例较低。可分四个解剖亚…
Meriem Mostefa-Kara, et al. Anatomy of the ventricular septal defect in congenital heart defects a random association. Orphanet Journal of Rare Diseases 2018 摘 要背景:室间隔缺损(VSD)是最常见的先…
Paul C. Tang, et al. Coronary Events in Patients Presenting for Repair of Acute Type A Aortic Dissection. AORTA 2017 摘 要 背景: 急性A型夹层患者术前常不做冠状动脉造影。我们对比了急性A型夹层修复患者和择期近端主动脉瘤修补术患者…